Small bowel infarction due to fibro muscular dysplasia: a case report and literature review
1 Russells Hall Hospital, Pensnett Road, Dudley, West Midlands, DY1 2HQ, UK
2 Mission of Mercy Hospital, Park Street, Kolkata, India
Cases Journal 2010, 3:79 doi:10.1186/1757-1626-3-79Published: 6 April 2010
We describe a rare case of small bowel infarction due to fibro muscular dysplasia in superior mesenteric artery in a young patient.
A 28 year old Asian female presented with acute onset left sided abdominal pain and watery diarrhea. She had a laparotomy due to further deterioration. It showed infracted small intestine, gall bladder and parts of liver. Abdomen had to be closed without any therapeutic procedure. She died in early post operative period. Autopsy showed fibro muscular dysplasia of superior mesenteric artery.
Fibro muscular dysplasia of SMA is rare, is treatable but has a high mortality.