Case Report
Recurrent retroperitoneal hemorrhage in a patient with tuberous sclerosis complex: a case report
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* Corresponding author: Massimo Chiarugi m.chiarugi@dc.med.unipi.it
1 Department of Surgery, University of Pisa, Pisa, PI, Italy
2 Department of Oncology, Transplantation and New Technologies, University of Pisa, Pisa, PI, Italy
3 Department of Surgery, University of Pisa, Santa Chiara Hospital, 67, Via Roma, 56100 Pisa, PI, Italy
Cases Journal 2008, 1:424 doi:10.1186/1757-1626-1-424
Published: 30 December 2008Abstract
Background
Tuberous sclerosis complex (TSC) is an autosomal dominant disorder. It is characterized by seizures, mental retardation and hamartomatous lesions, including facial angiofibroma, subependymal giant cell astrocytoma, cardiac rhabdomyoma and renal angiomyolipoma (AML). AMLs can bleed severely in the retroperitoneal space.
Case presentation
Herein, we present the case of a TSC patient presenting with recurrent severe episodes of retroperitoneal hemorrhage from AMLs successfully managed by angio-embolization.
Conclusion
Transarterial embolization is effective in preventing and controlling hemorrhage in patients with AMLs of the kidney